Zinner syndrome – a rare radiological diagnosis in a young male presenting with recurrent dysuria
Abstract
Zinner syndrome is a rare congenital abnormality of the mesonephric (Wolffian) duct consisting of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. The syndrome usually presents in the second or third decade of life mainly after the beginning of sexual activity and usually in the form of voiding manifestations. The main imaging modality is magnetic resonance imaging (MRI); however, usually suspected in transabdominal sonography, which may give initial clue to the diagnosis. Herein, we report a rare case of a 24 - year male with right renal agenesis with cystic pelvic mass diagnosed as Zinner syndrome via multimodality imaging.References
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11. Chen H-W, Huang S-C, Li Y-W, Chen S-J, Sheih C-P. Magnetic Resonance Imaging of Seminal Vesicle Cyst Associated with Ipsilateral Urinary Anomalies. J Formos Med Assoc. 2006;105(2):125–31.
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2. Nemec SF, Nemec U, Brugger PC, Bettelheim D, Weber M, Graham Jr. JM, et al. Male genital abnormalities in intrauterine growth restriction. Prenat Diagn. 2012 May 1;32(5):427–31.
3. Mehra S, Ranjan R, Garga UC. Zinner syndrome-a rare developmental anomaly of the mesonephric duct diagnosed on magnetic resonance imaging. Radiol case reports. 2016 May 24;11(4):313–7.
4. Soliman AA, Alshukami AA, AlZuber WH. Zinner’s syndrome, radiological diagnosis for a rare syndrome with non-specific clinical presentation: case report. Egypt J Radiol Nucl Med. 2020;51(1):217.
5. Sundar R, Sundar G. Zinner syndrome: an uncommon cause of painful ejaculation. BMJ Case Rep. 2015 Mar 6;2015:bcr2014207618.
6. Van den Ouden D, Blom J, Bangma C, de Spiegeleer A. Diagnosis and management of seminal vesicle cysts associated with ipsilateral renal agenesis: a pooled analysis of 52 cases. Eur Urol. 1998;33(5):433–40.
7. Abakar D, Badi F-E, Sabiri M, El Manjra S, Lezar S, Essodegui F. Zinner Syndrome. Eur J case reports Intern Med. 2021 Jun 3;8(7):2628.
8. Florim S, Oliveira V, Rocha D. Zinner syndrome presenting with intermittent scrotal pain in a young man. Radiol case reports. 2018 Sep 20;13(6):1224–7.
9. Juho Y-C, Wu S-T, Tang S-H, Cha T-L, Meng E. An Unexpected Clinical Feature of Zinner’s Syndrome– A Case Report. Urol Case Reports. 2015;3(5):149–51.
10. Khanduri S, Katyal G, Sharma H, Goyal A, Singh N, Yadav H. Unique Association of Multiple Seminal Vesicle Cysts with Contralateral Renal Agenesis: A Rare Variant of Zinner Syndrome. Cureus. 2017 Jul 1;9(7):e1415–e1415.
11. Chen H-W, Huang S-C, Li Y-W, Chen S-J, Sheih C-P. Magnetic Resonance Imaging of Seminal Vesicle Cyst Associated with Ipsilateral Urinary Anomalies. J Formos Med Assoc. 2006;105(2):125–31.
12. Trigaux J-P, Van Beers B, Delchambre F. Male genital tract malformations associated with ipsilateral renal agenesis: Sonographic findings. J Clin Ultrasound. 1991 Jan 1;19(1):3–10.
Published
2022-02-02
How to Cite
CHATAUT, Dinesh et al.
Zinner syndrome – a rare radiological diagnosis in a young male presenting with recurrent dysuria.
J Soc Surg Nep, [S.l.], v. 24, n. 2, p. 64-66, feb. 2022.
ISSN 2392-4772.
Available at: <https://jssn.org.np/index.php?journal=jssn&page=article&op=view&path%5B%5D=490>. Date accessed: 01 dec. 2023.
Section
Case Reports
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